The Congenital Diaphragmatic Hernia Study Group Registry

Francesco Morini; Pamela A. Lally; Kevin P. Lally; Pietro Bagolan

doi:10.1055/s-0035-1569151

European Journal of Pediatric Surgery, Table of Contents

Eur J Pediatr Surg 2015; 25(06): 488-496
DOI: 10.1055/s-0035-1569151

Review Article

Georg Thieme Verlag KG Stuttgart · New York

The Congenital Diaphragmatic Hernia Study Group Registry

Authors

Francesco Morini

¹Neonatal Surgery Unit, Department of Medical and Surgical Neonatology, Bambino Gesù Children's Hospital, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS), Rome, Italy
Pamela A. Lally

²Department of Pediatric Surgery, University of Texas Medical School at Houston and Children's Memorial Hermann Hospital, Houston, Texas, United States
Kevin P. Lally

²Department of Pediatric Surgery, University of Texas Medical School at Houston and Children's Memorial Hermann Hospital, Houston, Texas, United States
Pietro Bagolan

¹Neonatal Surgery Unit, Department of Medical and Surgical Neonatology, Bambino Gesù Children's Hospital, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS), Rome, Italy

Abstract

Congenital diaphragmatic hernia (CDH) is a rare anomaly with an incidence between 1/2,500 and 1/3,000 live births. The rarity of the disease makes it difficult to design powerful studies leading to accurate and meaningful evidence. For rare diseases, the development of multicenter international registries may help in collecting data and give an overall picture of the disease. In this review, we will describe the development of the CDH study group, we will describe its work methodology, and the results obtained since its birth in 1995.

Keywords

congenital diaphragmatic hernia - management - registry - stratification - treatment

Full Text

References

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