Spontaneous Haemophilia in a Female

E. H Braun; David B. Stollar

doi:10.1055/s-0038-1654520

Thrombosis and Haemostasis, Table of Contents

Thromb Haemost 1960; 4(03): 369-375
DOI: 10.1055/s-0038-1654520

Originalarbeiten — Original Articles — Travaux Originaux

Schattauer GmbH

Spontaneous Haemophilia in a Female

E. H Braun^*

,

David B. Stollar^**

Abstract

Summary

A case of haemophilia in a young white girl is described. There was a history of bleeding from birth. The thromboplastin generation test was grossly abnormal and A. H. G. levels were below 1%. Bleeding time and capillary morphology was within normal limits. Dental extraction after transfusion caused almost uncontrollable haemorrhage.

A complete family history was obtained for four generations. There was no case of a “bleeder” amongst these.

The girl’s apparent sex was confirmed by sex chromatin studies.

Full Text

References

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