Thrombosis and Haemostasis, Table of Contents Thromb Haemost 1965; 14(03/04): 332-340DOI: 10.1055/s-0038-1654872 Originalarbeiten — Original Articles — Travaux Originaux Schattauer GmbH A Case of Fibrin-Stabilizing Factor (FSF) Deficiency C. J Amris 1 From Department of Clinical Chemistry and Paediatric Department, University Hospital Copenhagen, Denmark , L Ranek 1 From Department of Clinical Chemistry and Paediatric Department, University Hospital Copenhagen, Denmark › Author Affiliations Recommend Article Abstract Buy Article Summary A case with congenital deficiency of fibrin-stabilizing factor is reported. Despite severe bleeding tendency the patient had a tonsillectomy and adenotomy without complications under cover of treatment with normal plasma. No familial disposition could be demonstrated. Full Text References References Amris G. J. Investigations concerning the protaminase activity in serum and plasma. Scand. J. clin. Lab. Invest. 14: 105 1962; Amris G. J, Amris A. The protaminase activity in normal individuals and in medical patients. Scand. J. clin. Lab. Invest. 14: 117 1962; Amris C. J, Amris A. Investigations concerning activator-free porcine plasmin. Scand. J. clin. Lab. Invest. 15: 189 1963; Amris C. J, Larsen V, Mogensen B, Storm O. Turnover and distribution of 13iodine-labelled porcine plasmin in man and dog. Dan. med. Bull. 11: 146 1964; Biggs R, Douglas A. S. The thromboplastin generation test. J. clin. Path. 06: 23 1953; Biggs R, Macfarlane R. G. Human Blood Coagulation and Its Disorders. Third Edit. Blackwell Scientific Publications; Oxford.: Duckert F, Jung E, Schmerling D. H. A hitherto undescribed congenital haemorrhagic diathesis probably due to fibrin stabilizing factor deficiency. Thrombos. Diathes. haemorrh. (Stuttg) 05: 179 1960; Gormsen J, Fleischer A. P. Fed. Proc. 22: 2400 1963; Hellem A. J. The adhesiveness of human blood platelets in vitro. Scand. J. clin. Lab. Invest. 12. suppl. 51 1960 Hicks N. D, Pitney W. R. A rapid screening test for disorders of thromboplastin generation. Brit. J. Haemat. 03: 227 1957; Ikkala E, Nevanlinna H. R. Congenital deficiency of fibrin stabilizing factor. Thrombos. Diathes. haemorrh. (Stuttg) 07: 567 1962; Jacobsson K. Studies on fibrinogen. Scand. J. clin. Lab. Invest. Suppl. 14, 1955 Josso F, Prou-Wartelle Alagille D, Soulier J. P. Le déficit congénital en Facteur Stabilisant de la Fibrine (Facteur XIII). Etude de deux cas. Nouv. Rev. franc. Hémat. 04: 267 1964; Laki K, Lorand L. On the solubility of fibrin clots. Science 108: 280 1948; Laki K. The polymerization of proteins: the action of thrombin on fibrinogen. Arch. Biochem. 32: 317 1951; Lorand L. Fibrin clots. Nature 166: 694 1950; Nilsson I. M, Blombäck M, von Francken I. On an inherited autosomal haemorrhagic diathesis with antihaemophilic globulin (AHG) deficiency and prolonged bleeding time. Acta med. scand. 159: 35 1957; Nilsson I. M, Olow B. Fibrinolysis induced by streptokinase in man. Acta chir. scand. 123: 247 1962; Mandelli F. Sindrome emorragica da difetto del Fattore stabilizzante fibrinico di Laki e Lorand. Med. clin. sper. 13: 175 1963; Masure R. Trouble congénital de l’hémostase associé à un deficit en Facteur Stabilisant de la Fibrine (F. S. F.). Hémostase. 03: 119 1963; Ollendorff P. Improvements in the thrombin generation test. Thrombos. Diathes. haemorrh. (Stuttg) 04: 244 1960; Owren P. A, Aas K. The control of dicumarol therapy and the quantitative determination of prothrombin and proconvertin. Scand. J. clin. Lab. Invest. 03: 201 1951; Quick A. J. On quantitative estimation of prothrombin. Amer. J. clin. Path. 15: 560 1945; Wolf P. A modification for routine laboratory use of Stefanini’s method of estimating factor V activity in human oxalated plasma. J. clin. Path. 06: 34 1953;
