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J Hand Microsurg 2020; 12(S 01): S64-S66
DOI: 10.1055/s-0039-1688680
Case Report

Carpometacarpal Arthroplasty and Ulnar Collateral Ligament Reconstruction in a Patient with Suspected Ehlers-Danlos Syndrome: A Case Report and Review of the Literature

Scott Samona
1   Christine M. Kleinert Institute for Hand and Microsurgery, Wixom, Michigan, United States
2   Christine M. Kleinert Institute for Hand and Microsurgery, Louisville, Kentucky, Unites States
,
Michelle Palazzo
2   Christine M. Kleinert Institute for Hand and Microsurgery, Louisville, Kentucky, Unites States
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Abstract

Ehlers-Danlos syndrome (EDS) is a disorder that presents with a heterogeneous constellation of symptoms, ranging from clinically silent to rapidly deteriorating. It is a multisystemic connective tissue disorder that may result in any number of manifestations, with joint hypermobility being a classic manifestation. We present a case of a 58-year-old woman, with suspected EDS, who presented with several years’ history of bilateral thumb pain, with imaging and physical examination findings consistent with bilateral thumb carpometacarpal (CMC) arthritis with metacarpophalangeal joint (MPJ) hypermobility. The Beighton hypermobility score was consistent with suspected EDS. Our patient underwent thumb CMC arthroplasty with ulnar collateral ligament (UCL) reconstruction.

Keywords

carpometacarpal arthritis - Ehlers-Danlos syndrome - ulnar collateral ligament


Publication History

Article published online:
02 June 2019

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