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Journal of Pediatric Neurology 2020; 18(05): 231-235
DOI: 10.1055/s-0039-1692139
DOI: 10.1055/s-0039-1692139
Case Report
Persistent Fetal Trigeminal Artery with Septopreoptic Holoprosencephaly: Report of an Unusual Association
Further Information
Publication History
03 January 2019
15 April 2019
Publication Date:
04 June 2019 (online)
![](https://www.thieme-connect.de/media/10.1055-s-00029030/202005/lookinside/thumbnails/10-1055-s-0039-1692139_1900001-1.jpg)
Abstract
Septopreoptic holoprosencephaly (HPE) is a type of HPE characterized by failure of separation of the septal and preoptic regions. Vascular anomalies associated with septopreoptic HPE include twig-like cerebral vessels and azygos anterior cerebral artery, the latter common to all forms of HPE. Here, we describe an 8-year-old boy presenting with developmental delay and abnormal movements who was found to have septopreoptic HPE associated with persistent trigeminal artery in magnetic resonance neuroimaging. This persistence of fetal trigeminal artery in HPE provides a further understanding of the pathogenesis of HPE.
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