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DOI: 10.1055/s-0041-1729921
Klippel–Trénaunay Syndrome and Developmental Coxa Vara in the Same Limb: A Case Report with a Review of the Literature
Funding We have not accepted any financial assistance from within or outside our institution for collecting data, writing the manuscript, or for its publications.
Abstract
We present a case of a 14-year-old girl who was first treated when she was 4 years old. She had progressive limping of the left lower limb from the age of 3 years. She was diagnosed to have developmental coxa vara of the left hip and treated by a subtrochanteric valgus osteotomy of the left femur. Later, she developed hypertrophy of the left upper and lower limbs. There were port-wine stains over the left lower limbs with multiple superficial varicosities. Her diagnosis was Klippel–Trénaunay syndrome (KTS). She is asymptomatic at the final follow-up. Both developmental coxa vara and KTS are rare conditions. We present this case to demonstrate the rarest combination of two rare conditions occurring in the same limb.
Keywords
Klippel–Trénaunay syndrome - developmental coxa vara - hypertrophy of limb - port-wine stainPublication History
Article published online:
30 July 2021
© 2021. International College of Angiology. This article is published by Thieme.
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