Kongenitaler Hyperinsulinismus

Der kongenitale Hyperinsulinismus ist die häufigste Ursache für eine persistierende Hypoglykämie-Neigung im frühen Kindesalter. Dieser Beitrag gibt einen praxisorientierten Überblick über Ursachen, Diagnosestellung und Therapie dieser Erkrankung.

Schlüsselwörter

hypoketotische Hypoglykämie - Hyperinsulinismus - Glukagon - Somatostatin - ABCC8 - KCNJ11

• Literatur

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