Aneurysmal Portosystemic Venous Shunt: A Case Report

Abstract

A case of an aneurysmal portosystemic venous shunt detected by colour Doppler ultrasound (CDUS) is presented. A young female patient complained of postprandial fatigue and had paroxysmal tachycardia. A direct vascular communication between right portal vein and right hepatic vein was found at CDUS and confirmed by direct portal angiogram. Using detachable coils a complete occlusion of the intrahepatic shunt was obtained. Reports from the literature regarding portovenous aneurysms are reviewed.

Eine junge Patientin berichtet über verstärkte postprandiale Müdigkeit und kurzzeitiges Herzrasen. Während der sonographischen Untersuchung wurde eine direkte Verbindung des rechten Pfortaderastes mit der rechten Lebervene entdeckt. Die portale Angiographie bestätigte den Befund. Mittels Spiralen wurde die vaskuläre Kurzschlußverbindung verschlossen. Literaturberichte bezüglich portovenöser systemischer Shuntverbindungen werden diskutiert.

Key words:

Colour Doppler sonography - Vascular malformation - Liver

Schlüsselwörter:

Farbkodierte Doppler-Sonographie - Gefäßmalformation - Leber

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