Download PDF
Semin Hear 2002; 23(3): 225-238
DOI: 10.1055/s-2002-34459
Copyright © 2002 by Thieme Medical Publishers, Inc., 333 Seventh Avenue, New York, NY 10001, USA. Tel.: +1(212) 584-4662

Developing a Multidisciplinary Clinical Protocol to Manage Pediatric Patients with Auditory Neuropathy

Kevin H. Franck, Dawne M. Rainey, Louise A. Montoya, Marsha Gerdes
  • The Center for Childhood Communication, The Children's Hospital of Philadelphia, Philadelphia, Pennsylvania
Further Information

Publication History

Publication Date:
02 October 2002 (online)

Also available at
    Permissions and Reprints

ABSTRACT

This article describes a multidisciplinary clinical protocol designed to address the audiologic, neurodevelopmental, and family support needs of infants and young children with auditory neuropathy at The Children's Hospital of Philadelphia. A multidisciplinary approach is necessary in this population because of the variable audiometric results and uncertain audiologic prognosis, a potential history of major neonatal illness with a high risk of neurodevelopmental delays, and the resulting parental stress. The protocol ensures consistency of recommendations and of clinical data across a large audiology staff. In addition, the protocol provides developmental monitoring and intervention by referral as necessary. Finally, the protocol addresses the mental health needs of families who face this diagnosis. This article also briefly describes our clinical experience to date with children diagnosed with auditory neuropathy.

KEYWORDS

Auditory neuropathy - clinical protocol - pediatric

REFERENCES

  • 1 Spoendlin H. Optic cochleovestibular degenerations in hereditary ataxias. II. Temporal bone pathology in two cases of Friedreich's ataxia with vestibulo-cochlear disorders.  Brain . 1974;  97 41-48
    CrossrefPubMedSearch in Google Scholar
  • 2 Amatuzzi M G, Northrop C, Liberman M C. Selective inner hair cell loss in premature infants and cochlea pathological patterns from neonatal intensive care unit autopsies.  Arch Otolaryngol Head Neck Surg . 2001;  127 629-636
    PubMedSearch in Google Scholar
  • 3 Starr A, Sininger Y, Winter M. Transient deafness due to temperature-sensitive auditory neuropathy.  Ear Hear . 1998;  19 169-179
    CrossrefPubMedSearch in Google Scholar
  • 4 Deltenre P, Mansbach A L, Bozet C. Auditory neuropathy with preserved cochlear microphonics and secondary loss of otoacoustic emissions.  Audiology . 1999;  38 187-195
    PubMedSearch in Google Scholar
  • 5 Rance G, Beer D E, Cone-Wesson B. Clinical findings for a group of infants and young children with auditory neuropathy.  Ear Hear . 1999;  20 238-252
    CrossrefPubMedSearch in Google Scholar
  • 6 Doyle K J, Sininger Y, Starr A. Auditory neuropathy in childhood.  Laryngoscope . 1998;  108 1374-1377
    CrossrefPubMedSearch in Google Scholar
  • 7 Berlin C I, Bordelon J, St John P. Reversing click polarity may uncover auditory neuropathy in infants.  Ear Hear . 1998;  19 37-47
    CrossrefPubMedSearch in Google Scholar
  • 8 Starr A, Picton T W, Sininger Y, Hood L J, Berlin C I. Auditory neuropathy.  Brain . 1996;  119 741-753
    CrossrefPubMedSearch in Google Scholar
  • 9 Shallop J K, Peterson A, Facer G W, Fabry L B, Driscoll C L. Cochlear implants in five cases of auditory neuropathy: postoperative findings and progress.  Laryngoscope . 2001;  111 555-562
    CrossrefPubMedSearch in Google Scholar
  • 10 Trautwein P G, Sininger Y S, Nelson R. Cochlear implantation of auditory neuropathy.  J Am Acad Audiol . 2000;  11 309-315
    PubMedSearch in Google Scholar
  • 11 Miyamoto R T, Kirk K I, Renshaw J, Hussain D. Cochlear implantation in auditory neuropathy.  Laryngoscope . 1999;  109 181-185
    CrossrefPubMedSearch in Google Scholar
  • 12 Palmer C V, Mormer E. Goals and expectations of the hearing aid fitting.  Trends Amplification . 1999;  4 61-71
    PubMedSearch in Google Scholar
  • 13 Robbins A M, Renshaw J J, Berry S W. Evaluating meaningful auditory integration in profoundly hearing-impaired children.  Am J Otol . 1991;  12(suppl) 144-150
    PubMedSearch in Google Scholar
  • 14 Moog J S, Geers A E. Early Speech Perception Test.  St. Louis, MO: Central Institute for the Deaf 1990
    Search in Google Scholar
  • 15 Elliott L L, Katz D R. Northwestern University-Children's Perception of Speech: Technical Manual.  St. Louis, MO: Auditec of St. Louis 1980
    Search in Google Scholar
  • 16 Ross M, Lerman J. A picture identification test for hearing impaired children.  J Speech Hear Res . 1970;  13 44-53
    CrossrefPubMedSearch in Google Scholar
  • 17 Seewald R. The desired sensation level method for fitting children.  Version 3.0 Hearing Journal . 1992;  45 26-36
    PubMedSearch in Google Scholar
  • 18 Bayley N. Bayley Scales of Infant Development, 2nd ed. San Antonio, TX: The Psychological Corporation, Harcourt Brace & Co; 1993 . 
  • 19 Baron-Cohen S, Allen J, Gillberg C. Can autism be detected at 18 months?.  <~>The needle, the haystack, and the CHAT. Br J Psychiatry . 1992;  161 839-843
    PubMedSearch in Google Scholar
  • 20 Vernon M. Parental reactions to birth-defective children.  Postgrad Med . 1979;  65 183-190
    PubMedSearch in Google Scholar
  • 21 Kazak A E, Simms S, Rourke M T. Family systems practice in pediatric psychology.  J Pediatr Psychol . 2002;  27 133-143
    CrossrefPubMedSearch in Google Scholar
  • 22 Meadow-Orlans K P, Mertens D M, Sass-Lehrer M A, Scott-Olson K. Support services for parents and their children who are deaf or hard of hearing. A national survey.  Am Ann Deaf . 1997;  142 278-288
    PubMedSearch in Google Scholar
  • 23 Micucci J A. The Adolescent in Family Therapy: Breaking the Cycle of Conflict and Control.  The Guilford Family Therapy Series. New York: Guildford Press 1998: 336
    Search in Google Scholar
  • 24 Corey G. Theory and Practice of Group Counseling, 3rd ed.  Pacific Grove, CA: Brooks/Cole 1989: 554
    Search in Google Scholar
  • 25 Orton G L. Strategies for Counseling with Children and Their Parents.  Pacific Grove, CA: Brooks/Cole 1997: 520
    Search in Google Scholar