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Endoscopy 2003; 35(10): 854-857
DOI: 10.1055/s-2003-42613
Case Report
© Georg Thieme Verlag Stuttgart · New York

Ampullary Carcinoid Tumor Presenting as Acute Pancreatitis in a Patient with von Recklinghausen’s Disease: Case Report and Review of the Literature

W.  Mayoral1 , J.  Salcedo1 , F.  Al-Kawas1
  • 1Division of Gastroenterology. Georgetown University Hospital, Washington, DC, USA
Further Information

Publication History

Submitted 16 November 2001

Accepted after Revision 21 March 2003

Publication Date:
10 October 2003 (online)

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A patient with von Recklinghausen syndrome presented with multiple attacks of pancreatitis. Evaluation using computed tomography, endoscopic retrograde cholangiopancreatography, and endosonography revealed an ampullary carcinoid.

The patient underwent a pylorus-sparing Whipple resection, and is doing well after 30 months of follow-up. This is the second reported case of ampullary carcinoid presenting with pancreatitis in a patient with von Recklinghausen syndrome.

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F. H. Al-Kawas, M.D.

Division of Gastroenterology, Georgetown University Hospital

3800 Reservoir Road, NW · Washington · DC 20007 · USA

Fax: +1-2027843957

Email: alkawasf@gunet.georgetown.edu