Zusammenfassung
Ein 9-jähriger Junge wurde mit einem tennisballgroßen subkutanen Tumor der Steißbeinregion
vorstellig. Das Alpha-Fetoprotein im Serum war nicht erhöht. Es erfolgte die Resektion
en bloc mit anhängender Steißbeinspitze. Die Histologie ergab ein myxopapilläres Ependymom.
Das myxopapilläre Ependymom kann metastasieren und lokal rezidivieren. Eine längerfristige
Nachbetreuung wird empfohlen.
Abstract
A 9-year-old boy was admitted with a circumscript subcutaneous tumor of the sacral
region. Serum alpha-fetoprotein was not elevated. The lesion was excised en bloc including
the top of the coccygis. Histology revealed a myxopapillary ependymoma without bony
involvement. Metastases were excluded. Extrasaspinal myxopapillary empendymoma is
a rare tumor of the sacrococcygeal region with a potential risk to develop metastases
and for local relapse. Long-term follow-up is recommended.
Schlüsselwörter
sakraler Tumor - sacrococcygeales Ependymom - extraspinales Ependymom - Steißbeinteratom
- Kindesalter
Key words
sacral tumor - sacrococcygeal ependymoma - extraspinal ependymoma - sacrococcygeal
teratoma - childhood
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Prof. Dr. med. Ralf-Bodo Tröbs
Kinderchirurgische Klinik · Marienhospital Herne
Widumer Str. 8
44627 Herne
Phone: +49/23 23/4 99 24 51
Fax: +49/23 23/49 93 28
Email: ralf-bodo.troebs@marienhospital-herne.de
