First Report of Distal Obstructive Uropathy and Prune-Belly Syndrome in an Infant with Amniotic Band Syndrome

Chih-Ping Chen; Fen-Fen Liu; Sheau-Wen Jan; Kuo-Gon Wang; Chung-Chi Lan

doi:10.1055/s-2007-994092

American Journal of Perinatology, Table of Contents

Am J Perinatol 1997; 14(1): 31-33
DOI: 10.1055/s-2007-994092

ORIGINAL ARTICLE

First Report of Distal Obstructive Uropathy and Prune-Belly Syndrome in an Infant with Amniotic Band Syndrome

Chih-Ping Chen¹ ^, ² , Fen-Fen Liu² , Sheau-Wen Jan² , Kuo-Gon Wang¹ , Chung-Chi Lan¹

¹Departments of Obstetrics and Gynecology, Mackay Memorial Hospital, Taipei, Taiwan, Republic of China
²Medical Research, Mackay Memorial Hospital, Taipei, Taiwan, Republic of China

Abstract

ABSTRACT

We describe the first report of distal obstructive uropathy and prune-belly syndrome in an infant with amniotic band syndrome. Prenatal ultrasonographic examination in the third trimester revealed intermittent oligohydramnios, bilateral hydronephrosis, and megacystis. Postnatally, the infant was found to have a scalp defect, a skin pedicle, pseudosyndactyly and constriction rings on the hands, marked distention of the abdomen, a fibrous band attached to the proximal urethra causing urethral stricture, a swollen penile shaft, bilateral talipes equinovarus, and syndactyly of the feet. Multiple fibrous amniotic bands could be identified in the placenta. Our case shows that fetal distal obstructive uropathy can be associated with the congenital constriction band syndrome.

Keywords

Distal obstructive uropathy - prune-belly syndrome - amniotic band syndrome

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