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Eur J Pediatr Surg 2009; 19(2): 124-125
DOI: 10.1055/s-2008-1038627
DOI: 10.1055/s-2008-1038627
Case Gallery
© Georg Thieme Verlag KG Stuttgart · New York
Exomphalos and Type IV Laryngeal Cleft: A Surgical Challenge
Further Information
Publication History
Publication Date:
11 February 2009 (online)
![](https://www.thieme-connect.de/media/ejps/200902/lookinside/thumbnails/10.1055-s-2008-1038627-1.jpg)
Introduction
A newborn infant was diagnosed with a giant exomphalos and a type IV laryngotracheoesophageal cleft (LTEC). Both disorders are associated with a high mortality and morbidity. Gastro-oesophageal reflux is common in patients with a cleft. The surgical challenges for fundoplication and gastrostomy included a shortened oesophagus, microgastria and abdominal wall mesh repair. Despite the complexities of this case, the infant continues to thrive.
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Dr. Jill Orford
Department of Paediatric Surgery
Princess Margaret Hospital for Children
Roberts Road
Subiaco, WA 6008
P.O. Box D184
Perth, WA 6840
Australia
Email: jillo@metabolicmedicine.com.au