Am J Perinatol 2008; 25(05): 265-270
DOI: 10.1055/s-2008-1075039
Original Article

Multidisciplinary Approach to Congenital Multiple Arterio-Porto-Caval Malformation: Case Report

Ali Gedikbasi
1   Department of Obstetrics and Gynecology, Perinatology Unit, Istanbul, Turkey
,
Kazim Oztarhan
2   Department of Pediatric Cardiology, Istanbul, Turkey
,
Bilge Sahin
3   Department of Pediatrics, Istanbul Bakirkoy Maternity and Children Diseases Hospital, Istanbul, Turkey
,
Banu Bingol
4   Department of Obstetrics and Gynecology, Istanbul Metropolitan Florence Nightingale Hospital, Istanbul, Turkey
,
Sebuh Kurugoglu
5   Department of Radiology, Pediatric Radiology, Istanbul, Turkey
,
Osman Faruk Senyuz
6   Department of Pediatric Surgery, Istanbul Cerrahpasa Medical Faculty, Istanbul, Turkey
,
Yavuz Ceylan
1   Department of Obstetrics and Gynecology, Perinatology Unit, Istanbul, Turkey
› Institutsangaben

Abstract

A case of intrahepatic arteriovenous malformation connected with umbilical, hepatic, portal, and arterial systems in a fetus diagnosed at 36 weeks of gestation is presented. Prenatal color Doppler ultrasonography in the fetal liver demonstrated complicated vascular connections fed by arterial and portal branches. Postnatal color Doppler, power Doppler, 3D power Doppler, abdominal multidetector computed tomography (MDCT), and angiography CT verified the prenatal diagnoses. Extended right hepatectomy was performed successfully on postnatal day 19.



Publikationsverlauf

Publikationsdatum:
02. April 2008 (online)

© 2008. Thieme Medical Publishers

Thieme Medical Publishers

 
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