Role of the OCT in the Diagnosis of Acute Zonal Occult Outer Retinopathy

Background

Gass introduced the acronym AZOOR (acute zonal occult outer retinopathy) in 1993 to describe a previously unrecognised retinal disease [3]. The primary abnormality appears to be a loss of the photoreceptor outer segment. The patients typically present themselves with central photopsia associated with progressive scotomata and blurring of vision. The fundus examination is initially unremarkable despite marked retinal dysfunction detectable electrophysiologically. After several months, the condition usually stabilises with later development of retinal pigment epithelial atrophy and intraretinal pigment migration corresponding to the zones of visual field loss. Bilateral involvement is frequent. A viral or autoimmune aetiology is suspected, but no cause is readily identifiable in this group of patients [2] [3] [4] [6].

References

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